Cap myopathy

Orpha code: 171881OMIM code: 609285

Definicja

Cap myopathy is a very rare congenital myopathy presenting a weakness of facial and respiratory muscles associated with craniofacial and thoracic deformities, as well as weakness of limb proximal and distal muscles. Onset is at birth or in childhood, weakness progression is slow but may lead to a severe and even fatal prognosis.

Disease data
Klasyfikacja

Disease

Synonimy
Cap disease
Choroba czapeczek
Kod ORPHA
171881
Kod OMIM
609285
Kod ICD10
G71.2
Kod ICD11
-

No additional description.

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