Lissencephaly due to TUBA1A mutation

Orpha code: 171680OMIM code: 611603

Definition

Lissencephaly (LIS) due to TUBA1A mutation is a congenital cortical development anomaly due to abnormal neuronal migration involving neocortical and hippocampal lamination, corpus callosum, cerebellum and brainstem. A large clinical spectrum can be observed, from children with severe epilepsy and intellectual and motor deficit to cases with severe cerebral dysgenesis in the antenatal period leading to pregnancy termination due to the severity of the prognosis.

Disease data
Classification

Malformation syndrome

ORPHA code
171680
OMIM code
611603
ICD10 code
Q04.3
ICD11 code
-

No additional description.

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