X-linked spastic paraplegia type 34

Orpha code: 171607OMIM code: 300750

Definicja

X-linked spastic paraplegia type 34 is a pure form of hereditary spastic paraplegia characterized by late childhood- to early adulthood-onset of slowly progressive spastic paraplegia with spastic gait and lower limb hyperreflexia, brisk tendon reflexes and ankle clonus. Lower limb pain and reduced lower limb vibratory sense is also reported in some older adult patients.

Disease data
Klasyfikacja

Disease

Synonimy
SPG34
SPG34
Kod ORPHA
171607
Kod OMIM
300750
Kod ICD10
G11.4
Kod ICD11
8B44.02

No additional description.

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