Primary sclerosing cholangitis

Orpha code: 171OMIM code: 613806

Definicja

Primary sclerosing cholangitis (PSC) is a rare, slowly progressive liver disease characterized by inflammation and destruction of the intra- and/or extra-hepatic bile ducts that lead to cholestasis, liver fibrosis, liver cirrhosis and ultimately liver failure.

Disease data
Klasyfikacja

Disease

Synonimy
PSC
PSC
Kod ORPHA
171
Kod OMIM
613806
Kod ICD10
K83.0
Kod ICD11
DB96.2

No additional description.

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