Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition Primary sclerosing cholangitis (PSC) is a rare, slowly progressive liver disease characterized by inflammation and destruction of the intra- and/or extra-hepatic bile ducts that lead to cholestasis, liver fibrosis, liver cirrhosis and ultimately liver failure. Disease data Classification Disease Synonyms PSC PSC ORPHA code 171 OMIM code 613806 ICD10 code K83.0 ICD11 code DB96.2 *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl