Description of the disease * EnglishPolish Pobierz sekcję do PDF Definicja A moderately severe form of hemophilia A characterized by factor VIII deficiency (biological activity between 1 and 5 IU/dL) leading to abnormal bleeding as a result of minor injuries, or following trauma, surgery or tooth extraction. Spontaneous hemorrhages are rare. The condition primarily affects males but may also be observed in female carriers of disease-causing mutations. Disease data Klasyfikacja Clinical subtype Synonimy Moderate congenital F8 deficiency Umiarkowanie ciężki Niedobór czynnika VIII Moderate congenital factor VIII deficiency Kod ORPHA 169805 Kod OMIM 306700 Kod ICD10 D66 Kod ICD11 3B10.0 *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl