Autosomal dominant centronuclear myopathy

Orpha code: 169189OMIM code: 160150

Definicja

A rare, autosomal dominant congenital myopathy characterized by numerous centrally placed nuclei on muscle biopsy and clinical features of a congenital myopathy (hypotonia, distal/proximal muscle weakness, rib cage deformities (sometimes associated with respiratory insufficiency), ptosis, ophthalmoparesis and weakness of the muscles of facial expression with dysmorphic facial features.

Disease data
Klasyfikacja

Disease

Synonimy
AD-CNM
AD-CNM
Kod ORPHA
169189
Kod OMIM
160150
Kod ICD10
G71.2
Kod ICD11
8C72.01

No additional description.

Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl