Description of the disease * EnglishPolish Pobierz sekcję do PDF Definicja Hereditary North American Indian childhood cirrhosis is a severe autosomal recessive intrahepatic cholestasis that has only been described in aboriginal children from northwestern Quebec. Manifesting first as transient neonatal jaundice, the disease evolves into periportal fibrosis and cirrhosis during a period ranging from childhood to adolescence. Disease data Klasyfikacja Clinical subtype Kod ORPHA 168583 Kod OMIM 604901 Kod ICD10 K74.6 Kod ICD11 DB93.20 *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl