Hereditary cryohydrocytosis with reduced stomatin

Orpha code: 168577OMIM code: 608885

Definition

A rare hemolytic anemia characterized by combination of neurologic features, such as psychomotor delay, seizures, variable movement disorders, and hemolytic anemia with stomatocytosis, resulting in cation-leaky erythrocytes, pseudohyperkalemia, hemolytic crises and hepatosplenomegaly. Cataracts are also a presenting feature.

Disease data
Classification

Disease

Synonyms
CHC type 2
CHC typu 2
Kriohydrocytoza dziedziczna typu 2
Kriohydrocytoza z niedoborem stomatyny
sdCHC
Hereditary cryohydrocytosis type 2
Stomatin-deficient cryohydrocytosis
sdCHC
ORPHA code
168577
OMIM code
608885
ICD10 code
D58.8
ICD11 code
3A10.Y

No additional description.

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