Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition Dentinogenesis imperfecta type 3 (DGI-3) is a rare, severe form of dentinogenesis imperfecta (DGI, see this term) characterized by opalescent primary and permanent teeth, marked attrition, large pulp chambers, multiple pulp exposure and shell teeth radiographically (i.e. teeth which appear hollow due to dentin hypotrophy). Disease data Classification Clinical subtype Synonyms Dentinogenesis imperfecta, Shields type 3 Dentinogenesis imperfecta, Shieldsa type 3 ORPHA code 166265 OMIM code 125500 ICD10 code K00.5 ICD11 code LA30.8 *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl