Dentinogenesis imperfecta type 3

Orpha code: 166265OMIM code: 125500

Definition

Dentinogenesis imperfecta type 3 (DGI-3) is a rare, severe form of dentinogenesis imperfecta (DGI, see this term) characterized by opalescent primary and permanent teeth, marked attrition, large pulp chambers, multiple pulp exposure and shell teeth radiographically (i.e. teeth which appear hollow due to dentin hypotrophy).

Disease data
Classification

Clinical subtype

Synonyms
Dentinogenesis imperfecta, Shields type 3
Dentinogenesis imperfecta, Shieldsa type 3
ORPHA code
166265
OMIM code
125500
ICD10 code
K00.5
ICD11 code
LA30.8

No additional description.

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