Dentinogenesis imperfecta type 3

Orpha code: 166265OMIM code: 125500

Definicja

Dentinogenesis imperfecta type 3 (DGI-3) is a rare, severe form of dentinogenesis imperfecta (DGI, see this term) characterized by opalescent primary and permanent teeth, marked attrition, large pulp chambers, multiple pulp exposure and shell teeth radiographically (i.e. teeth which appear hollow due to dentin hypotrophy).

Disease data
Klasyfikacja

Clinical subtype

Synonimy
Dentinogenesis imperfecta, Shields type 3
Dentinogenesis imperfecta, Shieldsa type 3
Kod ORPHA
166265
Kod OMIM
125500
Kod ICD10
K00.5
Kod ICD11
LA30.8

No additional description.

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