Autosomal dominant otospondylomegaepiphyseal dysplasia

Orpha code: 166100OMIM code: 184840

Definicja

A rare, genetic, multiple congenital anomalies/dysmorphic syndrome characterized by craniofacial dysmorphism (midface hypoplasia, depressed nasal bridge, small nose with upturned tip, cleft palate, Pierre Robin sequence), bilateral, pronounced sensorineural hearing loss, and skeletal/joint anomalies (including spondyloepiphyseal dysplasia, arthralgia/arthropathy), in the absence of ocular abnormalities.

Disease data
Klasyfikacja

Malformation syndrome

Synonimy
Stickler syndrome, nonocular type
AD OSMED
Stickler syndrome type 3
Stickler syndrome, non-ocular type
Kod ORPHA
166100
Kod OMIM
184840
Kod ICD10
Q87.0
Kod ICD11
-

No additional description.

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