Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition A form of von Willebrand disease (VWD) characterized by a bleeding disorder associated with a total or near-total absence of Willebrand factor (VWF) in the plasma and cellular compartments, also leading to a profound deficiency of plasmatic factor VIII (FVIII). It is the most severe form of VWD. Disease data Classification Clinical subtype Synonyms Choroba Willebranda typu 3 ORPHA code 166096 OMIM code 277480 ICD10 code D68.0 ICD11 code 3B12 *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl