Neutral lipid storage disease

Orpha code: 165OMIM code:

Definition

Neutral lipid storage disease (NLSD) refers to a group of diseases characterized by a deficit in the degradation of cytoplasmic triglycerides and their accumulation in cytoplasmic lipid vacuoles in most tissues of the body. The group is heterogeneous: currently cases of NLSD with icthyosis (NLSDI/Dorfman-Chanarin disease; see this term) and NLSD with myopathy (NLSDM/neutral lipid storage myopathy; see this term) can be distinguished.

Disease data
Classification

Clinical group

Synonyms
Lipidosis with triglyceride storage disease
Lipidoza z chorobą spichrzania triglicerydów
ORPHA code
165
OMIM code
-
ICD10 code
E75.5
ICD11 code
5C52.2

No additional description.

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