Acute myeloid leukemia and myelodysplastic syndromes related to radiation

Orpha code: 164726OMIM code:

Definicja

A subgroup of therapy-related myeloid neoplasms (t-MN), associated with treatment of an unrelated neoplastic disease with radiation. The neoplastic cells typically harbor unbalanced aberrations of chromosomes 5 and 7 (monosomy 5/del(5q) and monosomy 7/del(7q)) or a complex karyotype. Patients frequently present with multilineage dysplasia and cytopenias 5-10 years after exposure.

Disease data
Klasyfikacja

Disease

Synonimy
AML and myelodysplastic syndromes related to radiation
AML i zespoły mielodysplastyczne związane z promieniowaniem
Kod ORPHA
164726
Kod OMIM
-
Kod ICD10
D46.7
Kod ICD11
2A60.20

No additional description.

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