X-linked intellectual disability, Van Esch type

Orpha code: 163976OMIM code: 301030

Definition

A rare, genetic, syndromic intellectual disability characterized by developmental delay, mild to moderate intellectual disability, low birth weight, moderate to severe short stature, microcephaly and variable hypergonadotropic hypogonadism. Mild facial dismorfism include upslanted palpebral fissures and prominent nasal bridge.

Disease data
Classification

Malformation syndrome

ORPHA code
163976
OMIM code
301030
ICD10 code
Q87.8
ICD11 code
LD90

No additional description.

Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl