X-linked intellectual disability, Van Esch type

Orpha code: 163976OMIM code: 301030

Definicja

A rare, genetic, syndromic intellectual disability characterized by developmental delay, mild to moderate intellectual disability, low birth weight, moderate to severe short stature, microcephaly and variable hypergonadotropic hypogonadism. Mild facial dismorfism include upslanted palpebral fissures and prominent nasal bridge.

Disease data
Klasyfikacja

Malformation syndrome

Kod ORPHA
163976
Kod OMIM
301030
Kod ICD10
Q87.8
Kod ICD11
LD90

No additional description.

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