Cryptogenic late-onset epileptic spasms

Orpha code: 163708OMIM code:

Definicja

Cryptogenic late-onset epileptic spasms is a rare epilepsy syndrome characterized by late-onset (after 1 year old) epileptic spasms that ocurr in clusters, associated with tonic seizures, atypical absences and cognitive deterioration. Language difficulties and behavior problems are frequently present. EEG is characterized by a temporal, or temporofrontal, slow wave or spike focus combined with synchronous spike-waves and no hypsarrhythmia or background activity.

Disease data
Klasyfikacja

Disease

Synonimy
Late-onset infantile spasms
Drgawki dziecięce o późnym początku
Kod ORPHA
163708
Kod OMIM
-
Kod ICD10
G40.4
Kod ICD11
8A61.2Y

No additional description.

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