Cryptogenic late-onset epileptic spasms

Orpha code: 163708OMIM code:

Definition

Cryptogenic late-onset epileptic spasms is a rare epilepsy syndrome characterized by late-onset (after 1 year old) epileptic spasms that ocurr in clusters, associated with tonic seizures, atypical absences and cognitive deterioration. Language difficulties and behavior problems are frequently present. EEG is characterized by a temporal, or temporofrontal, slow wave or spike focus combined with synchronous spike-waves and no hypsarrhythmia or background activity.

Disease data
Classification

Disease

Synonyms
Late-onset infantile spasms
Drgawki dziecięce o późnym początku
ORPHA code
163708
OMIM code
-
ICD10 code
G40.4
ICD11 code
8A61.2Y

No additional description.

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