Distal monosomy 7q36

Orpha code: 1636OMIM code:

Definition

Distal monosomy 7q36 is a rare chromosomal anomaly syndrome, resulting from a partial deletion of the long arm of chromosome 7, with a highly variable phenotype typically characterized by holoprosencephaly, growth restriction, developmental delay, facial dysmorphism (facial clefts, prominent forehead, hypertelorism, low-set ears, flat and broad nasal bridge, large mouth), abnormal fingers and palm or sole creases, ocular abnormalities, and other congenital malformations (incl. genital anomalies and caudal deficiency sequence). Cardiopathies have been occasionally reported.

Disease data
Classification

Malformation syndrome

Synonyms
Distal deletion 7q36
Dystalna delecja 7q36
Monosomia 7qter
Telomerowa delecja 7q36
Monosomy 7qter
Telomeric deletion 7q36
ORPHA code
1636
OMIM code
-
ICD10 code
Q93.5
ICD11 code
-

No additional description.

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