Carnitine-acylcarnitine translocase deficiency

Orpha code: 159OMIM code: 212138

Definition

Carnitine-acylcarnitine translocase (CACT) deficiency is a life-threatening, inherited disorder of fatty acid oxidation which usually presents in the neonatal period with severe hypoketotic hypoglycemia, hyperammonemia, cardiomyopathy and/or arrhythmia, hepatic dysfunction, skeletal muscle weakness, and encephalopathy.

Disease data
Classification

Disease

Synonyms
CACT deficiency
Niedobór CACT
ORPHA code
159
OMIM code
212138
ICD10 code
E71.3
ICD11 code
5C52.00

No additional description.

Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl