Epidermolysis bullosa simplex with circinate migratory erythema

Orpha code: 158681OMIM code: 609352

Definition

A rare, inherited, epidermolysis bullosa simplex characterized by belt-like areas of erythema with multiple vesicles and small blisters at the advancing edge of erythema. The lesions occur on the limbs and trunk and heal with brown pigmentation but no scarring. Extracutaneous involvement is absent. Onset of the disease is usually at birth.

Disease data
Classification

Disease

Synonyms
EBS with circinate migratory erythema
Postać prosta pęcherzowego oddzielania się naskórka-wędrujący rumień
EBS-migr
ORPHA code
158681
OMIM code
609352
ICD10 code
Q81.0
ICD11 code
-

No additional description.

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