Acquired hemophagocytic lymphohistiocytosis associated with malignant disease

Orpha code: 158057OMIM code:

Definicja

A rare, secondary hemophagocytic lymphohistiocytosis characterized by occurring as either initial presentation of a malignant disease or at any stage during chemotherapy. The common associated malignancies are lukemias, B-cell, T-cell or NK-cell lymphomas, and Hodgkin lymphoma. Typical clinical manifestation includes fever, hepatosplenomegaly and cytopenias, combined with specific laboratory findings.

Disease data
Klasyfikacja

Particular clinical situation in a disease or syndrome

Kod ORPHA
158057
Kod OMIM
-
Kod ICD10
D76.1
Kod ICD11
3B62.Y

No additional description.

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