Indeterminate cell histiocytosis

Orpha code: 158019OMIM code:

Definition

A rare neoplastic disease characterized by multiple, and on occasion single, asymptomatic, smooth, red-brown papulonodules located on the face, neck, trunk and/or extremities which present a nonepidermotrophic histiocytic infiltrate with immunohistochemical features of both Langerhans and non-Langerhans cells (i.e. immunopositive for S100 protein and CD1a in the absence of Birbeck granules and langerin expression).

Disease data
Classification

Disease

Synonyms
Indeterminate dendritic cell neoplasm
Indeterminate dendritic cell tumor
ORPHA code
158019
OMIM code
-
ICD10 code
D76.3
ICD11 code
-

No additional description.

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