Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition Vici syndrome is a very rare and severe congenital multisystem disorder characterized by the principal features of agenesis of the corpus callosum, cataracts, oculocutaneous hypopigmentation, cardiomyopathy and combined immunodeficiency. Disease data Classification Malformation syndrome Synonyms Corpus callosum agenesis-cataract-immunodeficiency syndrome Zespół Dionisi, Viciego, Sabetta i Gambarara Dionisi-Vici-Sabetta-Gambarara syndrome ORPHA code 1493 OMIM code 242840 ICD10 code Q87.8 ICD11 code 4A01.1Y *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl