Univentricular heart

Orpha code: 1464OMIM code:

Definition

A severe congenital cardiac malformation characterized by both atria related entirely or almost entirely to one functionally single ventricular chamber. The clinical manifestations include congestive heart failure, failure to thrive, cyanosis, hypoxemia and neurodevelopmental disabilities.

Disease data
Classification

Morphological anomaly

Synonyms
Double inlet atrioventricular connection
Dwunapływowa lewa komora
ORPHA code
1464
OMIM code
-
ICD10 code
Q20.4
ICD11 code
LA89.0

No additional description.

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