Lynch syndrome

Orpha code: 144OMIM code: 614385

Definition

A rare inherited cancer-predisposing syndrome characterized by predisposition to a wide variety of cancers, including neoplasms of the digestive tract, urinary tract, kidney, endometrium, ovary, brain, and prostate, as well as sebaceous skin tumors, depending on the gene involved. Tumors may occur at any age but often arise in young people. Factors influencing individual tumor risk include sex, age, affected gene, and personal history of cancer.

Disease data
Classification

Disease

ORPHA code
144
OMIM code
614385
ICD10 code
D48.9
ICD11 code
-

No additional description.

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