Tessier number 7 facial cleft

Orpha code: 141276OMIM code: 613545

Definition

A rare lateral facial cleft characterized by a temporo-zygomatic defect, usually with absence of the zygomatic arch and deformities of the mandibular ramus, condyle, and coronoid process. Associated soft tissue abnormalities include malformations of the ear and hypoplasia or absence of the temporal muscle. Preauricular hair may be absent or divided into two portions. Facial manifestations include macrostomia (with extension of the cleft to the corner of the mouth) and pre-auricular tags. Incomplete clefts may be found in the molar region and between the maxillary tuberosity and pterygoid process.

Disease data
Classification

Morphological anomaly

Synonyms
Commissural facial cleft
Makrostomia
Rozszczep twarzy nr 7 wg klasyfikacji Tessiera
Transverse facial cleft
ORPHA code
141276
OMIM code
613545
ICD10 code
Q18.4
ICD11 code
LA51

No additional description.

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