Tessier number 4 facial cleft

Orpha code: 141258OMIM code: 600251

Definition

A rare oblique facial cleft characterized by a congenital unilateral or bilateral oculo-facial defect beginning at the upper lip lateral to the Cupid's bow, then running lateral to the nasal wing, to the lower eyelid lateral to the inferior punctum. Involvement of the facial skeleton begins between the lateral incisors and the canine tooth, involving the maxillary sinus, and ending at the infraorbital rim. Variable involvement of the eye can result in micro- or even anophthalmus.

Disease data
Classification

Morphological anomaly

ORPHA code
141258
OMIM code
600251
ICD10 code
Q18.8
ICD11 code
LA51

No additional description.

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