Nasal dermoid cyst

Orpha code: 141103OMIM code: 600679

Definition

A rare otorhinolaryngological malformation characterized by a dermoid cyst along the nasal dorsum or glabella, lined by keratinized squamous epithelium and containing intraluminal keratin and mature adnexal structures, such as hair follicles, sebaceous and sweat glands. The majority of nasal dermoid cysts are superficial, rarely they extend intracranially. The cysts are typically benign but are susceptible to recurrent infections that may progress to osteomyelitis, meningitis or an intracranial abscess.

Disease data
Classification

Morphological anomaly

Synonyms
Nasal dermoid sinus cyst
Torbiel skórzasta zatoki nosowej
ORPHA code
141103
OMIM code
600679
ICD10 code
Q18.8
ICD11 code
-

No additional description.

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