Third branchial cleft anomaly

Orpha code: 141030OMIM code:

Definition

A rare otorhinolaryngeal malformation characterized by a soft, fluctuant mass, abscess or draining tract along the anterior border of the lower half of sternocleidomastoid muscle, occasionally leading to development of retropharyngeal absces, acute suppurative thyroiditis, stridor, respiratory distress, odynophagia,and dysphagia. Anomaly occurs as a tract from the piriform sinus to the thyroid gland. A third branchial cleft fistula passes superficial to both the superior and recurrent laryngeal nerves, which is the main difference in comparison to the fourth branchial cleft fistula.

Disease data
Classification

Morphological anomaly

Synonyms
Third branchial cleft cyst
Przetoka trzeciego łuku skrzelowego
Torbiel trzeciego łuku skrzelowego
Third branchial cleft fistula
ORPHA code
141030
OMIM code
-
ICD10 code
Q18.0
ICD11 code
-

No additional description.

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