Description of the disease * EnglishPolish Pobierz sekcję do PDF Definicja A rare, medium or small vessel vasculitis characterized by focal and/or diffuse neurologic symptoms due to a documented arteritic process in the central nervous system, in the absence of other identified underlying cause (infectious, systemic, other neurologic diseases, etc.). It presents with non-specific symptoms of headache, stroke or transient ischemic attacks with cognitive impairment, hemiplegia, weakness, and rarely, with cranial nerve involvement, seizures and ataxia. Disease data Klasyfikacja Disease Synonimy Isolated angiitis of the central nervous system Izolowane zapalenie naczyń centralnego układu nerwowego PACNS PCNSV PACNS PCNSV Primary central nervous system vasculitis Primary vasculitis of the central nervous system Kod ORPHA 140989 Kod OMIM - Kod ICD10 I67.7 Kod ICD11 4A44.7 *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl