Congenital panfollicular nevus

Orpha code: 139414OMIM code:

Definition

Congenital panfollicular nevus is a rare, benign, skin tumor disorder characterized by the presence of congenital, large (few centimeters), elevated, well-circumscribed, pink-tan, multinodular, non-ulcerative, bosselated-surface skin lesions located on the neck, scalp or hand and which enlarge with time. Histologically, hamartomatous proliferation containing irregularly arranged, malformed hair follicles in various stages of development, surrounded by fibrous tissue and densely distributed within the dermis is observed.

Disease data
Classification

Disease

ORPHA code
139414
OMIM code
-
ICD10 code
I78.1
ICD11 code
-

No additional description.

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