Night blindness-skeletal anomalies-dysmorphism syndrome

Orpha code: 1390OMIM code:

Definicja

A rare, genetic, multiple congenital anomalies/dysmorphyc syndrome characterized by slowly progressive night blindness, skeletal abnormalities (sloping shoulders, joint hyperextensibility, minor radiological anomalies) and characteristic facial features (periorbital anomalies, malar flatness, retrognathia). Additional manifestations include myopia and extinguished electroretinograms. There have been no further descriptions in the literature since 1979.

Disease data
Klasyfikacja

Malformation syndrome

Synonimy
Hunter-Thompson-Reed syndrome
Zespół Huntera, Thompsona i Reeda
Kod ORPHA
1390
Kod OMIM
-
Kod ICD10
Q87.8
Kod ICD11
-

No additional description.

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