Auriculocondylar syndrome

Orpha code: 137888OMIM code: 615706

Definicja

A rare, genetic dysostosis with predominant craniofacial involvement characterized by bilateral external ear malformations, mandibular condyle hypoplasia, microstomia, micrognathia, microglossia and facial asymmetry. Additional manifestations include hypotonia, ptosis, cleft palate, full cheeks, developmental delay, hearing impairment and respiratory distress. Significant intra- and interfamilial phenotypic variation has been reported.

Disease data
Klasyfikacja

Malformation syndrome

Synonimy
Question mark ear syndrome
Question mark ear syndrome
Kod ORPHA
137888
Kod OMIM
615706
Kod ICD10
Q75.8
Kod ICD11
LD2F.16

No additional description.

Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl