Pellucid marginal degeneration

Orpha code: 137672OMIM code:

Definition

A rare disorder of the anterior segment of the eye characterized by slowly progressive, bilateral, non-ulcerative, non-inflammatory, clear thinning of the inferior portion of the peripheral cornea (extending from the 4 o'clock to the 8 o'clock position), with an area of corneal protrusion above the point of maximal thinning, resulting in against-the-rule astigmatism with decreased visual acuity. The central cornea is of normal thickness.

Disease data
Classification

Disease

ORPHA code
137672
OMIM code
-
ICD10 code
H18.7
ICD11 code
9A78.4

No additional description.

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