Nephrogenic systemic fibrosis

Orpha code: 137617OMIM code:

Definicja

Nephrogenic systemic fibrosis (NSF) is a rare systemic fibrosing condition observed in renally impaired patients and characterized by a hardening and thickening of the skin with fibrotic plaques or papules, pruritus, joint pain and stiffness, muscle weakness, limitation of range of motion, and yellowed eyes. It is generally associated with administration of gadolinium-based magnetic resonance imaging contrast agents (GBCA) in patients with kidney disease.

Disease data
Klasyfikacja

Disease

Synonimy
Nephrogenic fibrosing dermopathy
Nefrogenna dermopatia włóknista
Kod ORPHA
137617
Kod OMIM
-
Kod ICD10
L98.8
Kod ICD11
FB51.Y

No additional description.

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