Carnosinase deficiency

Orpha code: 1361OMIM code: 212200

Definicja

A rare inborn error of metabolism characterized by low serum carnosinase activity, persistent carnosinuria, and carnosinemia. The clinical phenotype is highly variable, with some patients remaining asymptomatic, while others have been reported to show severe developmental delay, intellectual disability, hypotonia, seizures, and other neurological signs and symptoms.

Disease data
Klasyfikacja

Biological anomaly

Synonimy
Deficyt karnozydazy
Kod ORPHA
1361
Kod OMIM
212200
Kod ICD10
E70.8
Kod ICD11
5C50.F1

No additional description.

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