Larynx atresia

Orpha code: 1202OMIM code: 150300

Definicja

A rare larynx anomaly characterized by complete absence of the laryngeal lumen resulting in congenital upper airway obstruction syndrome which, without fetal or neonatal intervention, is incompatible with life. Fetal sonography shows a dilated trachea, hyperechoic lungs, pleural effusion, minimal fetal abdominal ascites or hydrops, and amniotic fluid abnormalities.

Disease data
Klasyfikacja

Malformation syndrome

Kod ORPHA
1202
Kod OMIM
150300
Kod ICD10
Q31.8
Kod ICD11
LA71.Y

No additional description.

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