Spastic ataxia with congenital miosis

Orpha code: 1182OMIM code: 108650

Definition

Spastic ataxia with congenital miosis is a rare hereditary ataxia characterized by an apparently non-progressive or slowly progressive symmetrical ataxia of gait, pyramidal signs in the limbs, spasticity and hyperreflexia (especially in the lower limbs) together with dysarthria and impaired pupillary reaction to light, presenting as a fixed miosis (with pupils that seldom exceed 2 mm in diameter and dilate poorly with mydriatics). Nystagmus may also be present.

Disease data
Classification

Disease

Synonyms
Autosomal dominant spastic ataxia type 7
SPAX7
Autosomalna dominująca ataksja spastyczna typu 7
SPAX7
ORPHA code
1182
OMIM code
108650
ICD10 code
G11.4
ICD11 code
-

No additional description.

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