Bartter syndrome

Orpha code: 112OMIM code: 300971

Definition

Bartter syndrome is a group of rare renal tubular disease characterized by impaired salt reabsorption in the thick ascending limb of Henle's loop and clinically by the association of hypokalemic alkalosis, hypercalciuria/nephrocalcinosis, increased levels of plasma renin and aldosterone, low blood pressure and vascular resistance to angiotensin II.

Disease data
Classification

Disease

Synonyms
Renal tubular normotensive hypokalemic alkalosis with hypercalciuria
Kanalikowa zasadowica hipokaliemiczna normotensyjna z hiperkalciurią
Tubulopatia z utratą soli, typu pętli Henlego
Salt-losing tubular disorder, Henle's loop type
Salt-wasting tubulopathy, Henle's loop type
ORPHA code
112
OMIM code
300971
ICD10 code
E26.8
ICD11 code
GB90.43

No additional description.

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