Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition A rare, genetic, congenital limb malformation syndrome characterized by bilateral thumb ankylosis, type A brachydactyly and mild to moderate intellectual disability. Patients present thumb stiffness and abnormalities of the metacarpal bones, frequently associated with mild facial dysmorphism and signs of obesity. There have been no further descriptions in the literature since 1990. Disease data Classification Malformation syndrome Synonyms Piussan-Lenaerts-Mathieu syndrome Zespół Piussana, Lenaertsa i Mathieu ORPHA code 1078 OMIM code 188201 ICD10 code Q87.2 ICD11 code - *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl