Leiomyosarcoma of small intestine

Orpha code: 104076OMIM code:

Definition

Small bowel leiomyosarcoma is a rare type of small bowel malignancy, originating in the smooth muscle cells within the muscularis propria or the muscularis mucosa, most often found in the jejunum, and presenting with gastrointestinal bleeding and anemia and sometimes with other non-specific symptoms such as vomiting, nausea, abdominal pain and weakness and spreading to regional lymph nodes in 14% of cases.

Disease data
Classification

Disease

ORPHA code
104076
OMIM code
-
ICD10 code
C17.0
ICD11 code
-

No additional description.

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