Autoimmune pancreatitis

Orpha code: 103919OMIM code:

Definition

A rare pancreatic disease characterized by chronic non-alcoholic pancreatitis that presents with abdominal pain, steatorrhea, obstructive jaundice and responds well to steroid therapy and is seen in two subforms: type which affects elderly males, involves other organs and has increased immunoglobin G4 (IgG4) levels and type 2 which affects both sexes equally but presents at a younger age and has no other organ involvement or increased IgG4 levels.

Disease data
Classification

Clinical group

Synonyms
AIP
AIP
ORPHA code
103919
OMIM code
-
ICD10 code
K86.1
ICD11 code
DC33

No additional description.

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