Trehalase deficiency

Orpha code: 103909OMIM code: 612119

Definition

A rare, genetic, intestinal disease characterized by osmotic diarrhea, abdominal pain and increased rectal flatulence after ingestion of trehalose, a disaccharide found mainly in mushrooms, due to intestinal trehalase deficiency. It occurs primarily in the Greenland population, although cases have also been reported elsewhere.

Disease data
Classification

Disease

Synonyms
Isolated trehalose intolerance
Izolowana nietolerancja trehalozy
ORPHA code
103909
OMIM code
612119
ICD10 code
E74.3
ICD11 code
5C61.3

No additional description.

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