Jejunal neuroendocrine tumor

Orpha code: 100077OMIM code:

Definition

Jejunal neuroendocrine tumor is a rare, primary, malignant, epithelial neoplasm of the small intestine arising from enterochromaffin cells in the jejunum. Clinical behavior depends on the histologic grade, but initially it is generally characterized by vague abdominal symptoms (cramping, bloating, diarrhea) with insidious onset, although sometimes it could present with signs of bowel obstruction/perforation or gastrointestinal bleeding. Diagnosis in advanced stages with regional or distant spread is common, but signs of carcinoid syndrome (flushing, sweating, diarrhea) are usually not apparent until hepatic metastasis has occurred.

Disease data
Classification

Category

Synonyms
Jejunal neuroendocrine neoplasm
Nowotwór neuroendokrynny jelita czczego
ORPHA code
100077
OMIM code
-
ICD10 code
-
ICD11 code
-

No additional description.

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