Extraneural perineurioma

Orpha code: 100002OMIM code:

Definicja

Extraneural perineurioma is a rare tumor of cranial and spinal nerves arising from peripheral nerve sheet and composed exclusively or predominantly of cells showing perineurial differentiation. It presents as a well-circumscribed, rarely encapsulated mass, not associated with a recognizable nerve, most commonly arising in the dermis and subcutis of the extremities or trunk, or, rarely, in deep soft tissue or skin (e.g., in the stomach, kidney, pancreas, maxillary sinus, mandible, bronchial tree and the face). The clinical presentation depends on the localization.

Disease data
Klasyfikacja

Disease

Synonimy
Soft tissue perineurioma
Guz okołonerwowy/Onerwiak tkanek miękkich
Kod ORPHA
100002
Kod OMIM
-
Kod ICD10
D36.1
Kod ICD11
-

No additional description.

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