Guz neuroendokrynny trzustki

Kod Orpha: 97253Kod OMIM:

Definicja

Pancreatic endocrine tumor, also known as pancreatic neuroendocrine tumor (PNET), describes a group of endocrine tumors originating in the pancreas that are usually indolent and benign, but may have the potential to be malignant. They can be functional, exhibiting a hormonal hypersecretion syndrome, but can be non-functional presenting with non-specific symptoms and include insulinoma, glucagonoma, VIPoma, somatostatinoma (SSoma), PPoma and Zollinger-Ellison syndrome (ZES, or gastrinoma) and other ectopic hormone producing tumors (such as GRFoma) (see these terms).

Dane
Klasyfikacja

Kategoria

Synonimy
PNET
Pancreatic NET
Pancreatic neuroendocrine tumor
Well-differentiated NEN of pancreas
Well-differentiated neuroendocrine neoplasm of pancreas
Well-differentiated pancreatic NEN
Well-differentiated pancreatic neuroendocrine neoplasm
PNET
Pancreatic NET
Pancreatic neuroendocrine tumor
Well-differentiated NEN of pancreas
Well-differentiated neuroendocrine neoplasm of pancreas
Well-differentiated pancreatic NEN
Well-differentiated pancreatic neuroendocrine neoplasm
Kod ORPHA
97253
Kod OMIM
-
Kod ICD10
E16.8
Kod ICD11
2C10.1

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