Atypowy liszaj śluzowaty

Kod Orpha: 86797Kod OMIM:

Definicja

An intermediate form of lichen myxedematosus (LM) (a form of mucin dermal deposit) which does not meet the criteria for either scleromyxedema or the localized form. Three clinical subtypes have been described and include scleromyxedema without monoclonal gammopathy; localized forms with monoclonal gammopathy and/or systemic symptoms; localized forms with mixed features of the 5 subtypes of localized LM (discrete form, acral persistent papular mucinosis, self-healing papular mucinosis, papular mucinosis of infancy, and a pure nodular form). The course of atypical LM is unpredictable because only a few cases have been reported.

Dane
Klasyfikacja

Choroba

Synonimy
Intermediate lichen myxedematosus
Liszaj śluzowaty średniozaawanowany
Kod ORPHA
86797
Kod OMIM
-
Kod ICD10
L98.5
Kod ICD11
EB90.1Y

Brak opisu rozszerzonego dla tej choroby. Opracowanie w toku.

Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl