Rozlana mastocytoza skórna

Kod Orpha: 79456Kod OMIM:

Definicja

Diffuse cutaneous mastocytosis (DCM) is a rare form of cutaneous mastocytosis (CM; see this term) characterized by generalized erythroderma, various degrees of blistering, skin with a ''peau d'orange'' appearance and the accumulation of mast cells in the skin. At least two DCM variants are recognized, one with extreme blistering (Bullous DCM; see this term) and one with infiltrations (Pseudoxanthomatous DCM; see this term).

Dane
Klasyfikacja

Choroba

Synonimy
DCM
DCM
Diffuse cutaneous maculopapulous mastocytosis
Diffuse cutaneous maculopapulous mastocytosis
Kod ORPHA
79456
Kod OMIM
-
Kod ICD10
Q82.2
Kod ICD11
2A21.1Y

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