Elastosis perforans serpiginosa

Kod Orpha: 79148Kod OMIM: 130100

Definicja

A rare acquired dermis elastic tissue disorder with increased elastic tissue characterized by focal dermal elastosis and transepidermal elimination of abnormal elastic fibers, presenting as small keratotic papules or plaques arranged in groups in serpiginous or annular patterns on the neck, face, and arms, while other areas are less frequently affected. Although spontaneous regression is possible, the lesions often persist over longer periods of time. The condition typically occurs during childhood or early adulthood and is more frequent in men than in women.

Dane
Klasyfikacja

Choroba

Kod ORPHA
79148
Kod OMIM
130100
Kod ICD10
L87.2
Kod ICD11
EE70.Y

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