Dyskeratoma brodawkowata

Kod Orpha: 69745Kod OMIM:

Definicja

A rare, benign, epidermal disease characterized by a solitary, asymptomatic, verrucous, skin-coloured to red-brown papule or nodule, which contains a central pore and keratotic plug, occuring most frequently on the scalp, face and neck (rarely, in the mouth, under the nail plate or on the mons pubis). Occasionally, lesions may be multiple and/or pruritic. Histologically, a well-circumscribed, cup-shaped, keratin-filled invagination, with prominent acantholytic dyskeratosis, suprabasilar clefts and villi projecting into the clefts, is observed.

Dane
Klasyfikacja

Choroba

Synonimy
Follicular dyskeratoma
Dyskeratoma pęcherzykowa
Kod ORPHA
69745
Kod OMIM
-
Kod ICD10
L85.8
Kod ICD11
2F21.Y

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