Opis choroby * EnglishPolish Pobierz sekcję do PDF Definicja A rare vascular skin disease characterized by recurrent focal non-inflammatory thrombosis of dermal venulae, predominantly of the lower extremities, resulting in a cutaneous response manifested as pruritus and painful papules and erythematous plaques. The lesions evolve into hemorrhagic vesicles or bullae, which rupture and turn into painful ulcers merging into reticulate, confluent, geometric, and painful ulcerations. During a period of a few months, the ulcerations change to porcelain-white atrophic scars with punctate telangiectasia (so-called atrophie blanche). In active disease, lesions in different stages coexist. Dane Klasyfikacja Zespół kliniczny Synonimy Livedo reticularis with summer ulcerations Milian atrophie blanche Segmental hyalinizing vasculitis Livedo reticularis with summer ulcerations Milian atrophie blanche Segmental hyalinizing vasculitis Kod ORPHA 542643 Kod OMIM - Kod ICD10 L95.0 Kod ICD11 EF50 *Źródło Rozszerzony opis choroby Pobierz sekcję do PDF Brak opisu rozszerzonego dla tej choroby. Opracowanie w toku. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl