Waskulopatia sinicza

Kod Orpha: 542643Kod OMIM:

Definicja

A rare vascular skin disease characterized by recurrent focal non-inflammatory thrombosis of dermal venulae, predominantly of the lower extremities, resulting in a cutaneous response manifested as pruritus and painful papules and erythematous plaques. The lesions evolve into hemorrhagic vesicles or bullae, which rupture and turn into painful ulcers merging into reticulate, confluent, geometric, and painful ulcerations. During a period of a few months, the ulcerations change to porcelain-white atrophic scars with punctate telangiectasia (so-called atrophie blanche). In active disease, lesions in different stages coexist.

Dane
Klasyfikacja

Zespół kliniczny

Synonimy
Livedo reticularis with summer ulcerations
Milian atrophie blanche
Segmental hyalinizing vasculitis
Livedo reticularis with summer ulcerations
Milian atrophie blanche
Segmental hyalinizing vasculitis
Kod ORPHA
542643
Kod OMIM
-
Kod ICD10
L95.0
Kod ICD11
EF50

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