Torbiel tętniakowata kości

Kod Orpha: 480553Kod OMIM:

Definicja

A rare bone tumor characterized by a benign, cystic lesion consisting of blood-filled cavities divided by fibrous septa containing fibroblasts, multinucleated osteoclast-type giant cells, and reactive woven bone. The tumor may arise <i>de novo</i> or secondarily, complicating other benign or malignant bone tumors. It most commonly arises during the first two decades of life and often affects the epiphyses of long bones and posterior elements of vertebral bodies. Patients typically present with pain and swelling, or neurological symptoms due to compression of nerve roots or the spinal cord by vertebral tumors.

Dane
Klasyfikacja

Choroba

Kod ORPHA
480553
Kod OMIM
-
Kod ICD10
M85.5
Kod ICD11
FB80.6

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